Department of Gastroenterological Surgery, Kochi Health Sciences Center
2
Department of Gastroenterological Surgery, Okayama University
Background: Clinicopathological characteristics of intraductal papillary mucinous neoplasm (IPMN) derived from the ectopic pancreas have not been elucidated owing to its rarity. Methods: MEDLINE databases from 1985 to 2021 were searched. Data regarding patient characteristics, diagnostic modalities, treatment, and prognosis were extracted from the identified articles.Results: Comprehensive data on 13 patients (10 men and three women) with IPMN derived from ectopic pancreas were extracted. The median age was 69 years (range, 42 to 80 years). The tumors were located in the stomach in six patients, the duodenum in one patient, jejunum in three patients, ileum in one patient, and Meckel’s diverticulum in two patients. Histopathological examination revealed IPMN in 10 patients and intraductal papillary mucinous carcinoma (IPMC) in three patients. The median size of the tumor was not significantly different between the IPMC group and the IPMN group (P = 0.611).Conclusions: Accurate preoperative diagnosis and differential diagnosis between IPMN and IPMC remain difficult despite recent advances in imaging modalities.
Index Term 1: intraductal papillary mucinous neoplasm